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Sporadic segmental Interstitial cell of cajal hyperplasia (microscopic GIST) with unusual diffuse longitudinal growth replacing the muscularis propria: differential diagnosis to hereditary GIST syndromes

Gastrointestinal stromal tumors (GIST) usually form a well-circumscribed mass. However, patients with germline mutations in c-KIT, PDGFRA and NF1 may present with diffuse interstitial cell of Cajal (ICC) hyperplasia along the Auer-bach plexus without forming a discrete mass. To our knowledge, sporad...

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Autores principales: Agaimy, Abbas, Märkl, Bruno, Arnholdt, Hans, Hartmann, Arndt, Schneider-Stock, Regine, Chetty, Runjan
Formato: Artigo
Lenguaje:Inglês
Publicado: e-Century Publishing Corporation 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2897106/
https://ncbi.nlm.nih.gov/pubmed/20606738
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