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Ion-abrasion scanning electron microscopy reveals distorted liver mitochondrial morphology in murine methylmalonic acidemia

Methylmalonic acidemia is a lethal inborn error of metabolism that causes mitochondrial impairment, multi-organ dysfunction and a shortened lifespan. Previous transmission electron microscope studies of thin sections from normal (Mut(+/+)) and diseased (Mut (−/−)) tissue found that the mitochondria...

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Autori principali: Murphy, Gavin E., Lowekamp, Bradley C., Zerfas, Patricia M., Chandler, Randy J., Venditti, Charles P., Subramaniam, Sriram
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2010
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2885563/
https://ncbi.nlm.nih.gov/pubmed/20399866
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jsb.2010.04.005
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