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Diamond Blackfan Anemia at the Crossroad between Ribosome Biogenesis and Heme Metabolism

Diamond-Blackfan anemia (DBA) is a rare, pure red-cell aplasia that presents during infancy. Approximately 40% of cases are associated with other congenital defects, particularly malformations of the upper limb or craniofacial region. Mutations in the gene coding for the ribosomal protein RPS19 have...

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Autores principales: Chiabrando, Deborah, Tolosano, Emanuela
Formato: Artigo
Lenguaje:Inglês
Publicado: Hindawi Publishing Corporation 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2864449/
https://ncbi.nlm.nih.gov/pubmed/20454576
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2010/790632
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