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Development of Disseminated Histiocytic Sarcoma in a patient with Autoimmune Lymphoproliferative Syndrome (ALPS) and Associated Rosai-Dorfman Disease
Patients with autoimmune lymphoproliferative syndrome (ALPS) have defective lymphocyte apoptosis, with increased risk for lymphoid malignancies. Herein, we report a patient with ALPS who developed histiocytic sarcoma in a background of sinus histiocytosis and massive lymphadenopathy (SHML) or Rosai-...
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| Главные авторы: | , , , , |
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| Формат: | Artigo |
| Язык: | Inglês |
| Опубликовано: |
2010
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| Предметы: | |
| Online-ссылка: | https://ncbi.nlm.nih.gov/pmc/articles/PMC2861546/ https://ncbi.nlm.nih.gov/pubmed/20216376 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/PAS.0b013e3181d5ddf8 |
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