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Development of Disseminated Histiocytic Sarcoma in a patient with Autoimmune Lymphoproliferative Syndrome (ALPS) and Associated Rosai-Dorfman Disease

Patients with autoimmune lymphoproliferative syndrome (ALPS) have defective lymphocyte apoptosis, with increased risk for lymphoid malignancies. Herein, we report a patient with ALPS who developed histiocytic sarcoma in a background of sinus histiocytosis and massive lymphadenopathy (SHML) or Rosai-...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Venkataraman, Girish, McClain, Kenneth L., Pittaluga, Stefania, Rao, V. Koneti, Jaffe, Elaine S.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2010
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC2861546/
https://ncbi.nlm.nih.gov/pubmed/20216376
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/PAS.0b013e3181d5ddf8
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