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Dysferlin Interacts with Tubulin and Microtubules in Mouse Skeletal Muscle

Dysferlin is a type II transmembrane protein implicated in surface membrane repair in muscle. Mutations in dysferlin lead to limb girdle muscular dystrophy 2B, Miyoshi Myopathy and distal anterior compartment myopathy. Dysferlin's mode of action is not well understood and only a few protein bin...

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Autors principals: Azakir, Bilal A., Di Fulvio, Sabrina, Therrien, Christian, Sinnreich, Michael
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2010
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2853571/
https://ncbi.nlm.nih.gov/pubmed/20405035
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0010122
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