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Maintenance of Glomerular Filtration Barrier Integrity Requires Laminin α5

Mutation of the mouse laminin α5 gene results in a variety of developmental defects, including defects in kidney structure and function. Whereas the total absence of laminin α5 results in breakdown of the glomerular basement membrane (GBM) and failed glomerular vascularization, a hypomorphic Lama5 m...

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Autores principales: Goldberg, Seth, Adair-Kirk, Tracy L., Senior, Robert M., Miner, Jeffrey H.
Formato: Artigo
Lenguaje:Inglês
Publicado: American Society of Nephrology 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2844312/
https://ncbi.nlm.nih.gov/pubmed/20150535
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1681/ASN.2009091004
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