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Microarchitecture Is Severely Compromised but Motor Protein Function Is Preserved in Dystrophic mdx Skeletal Muscle

Progressive force loss in Duchenne muscular dystrophy is characterized by degeneration/regeneration cycles and fibrosis. Disease progression may involve structural remodeling of muscle tissue. An effect on molecular motorprotein function may also be possible. We used second harmonic generation imagi...

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Autors principals: Friedrich, O., Both, M., Weber, C., Schürmann, S., Teichmann, M.D.H., von Wegner, F., Fink, R.H.A., Vogel, M., Chamberlain, J.S., Garbe, C.
Format: Artigo
Idioma:Inglês
Publicat: The Biophysical Society 2010
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2820646/
https://ncbi.nlm.nih.gov/pubmed/20159157
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bpj.2009.11.005
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