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Genetic modeling of Li-Fraumeni syndrome in zebrafish

Li-Fraumeni syndrome (LFS) is a highly penetrant, autosomal dominant, human familial cancer predisposition. Although a key role for the tumor suppressor p53 has been implicated in LFS, the genetic and cellular mechanisms underpinning this disease remain unknown. Therefore, modeling LFS in a vertebra...

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Autori principali: Parant, John M., George, Stephen A., Holden, Joseph A., Yost, H. Joseph
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Company of Biologists Limited 2010
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2806900/
https://ncbi.nlm.nih.gov/pubmed/20075382
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1242/dmm.003749
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