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Human voltage-gated sodium channel mutations that cause inherited neuronal and muscle channelopathies increase resurgent sodium currents

Inherited mutations in voltage-gated sodium channels (VGSCs; or Nav) cause many disorders of excitability, including epilepsy, chronic pain, myotonia, and cardiac arrhythmias. Understanding the functional consequences of the disease-causing mutations is likely to provide invaluable insight into the...

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Autors principals: Jarecki, Brian W., Piekarz, Andrew D., Jackson, James O., Cummins, Theodore R.
Format: Artigo
Idioma:Inglês
Publicat: American Society for Clinical Investigation 2009
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2799199/
https://ncbi.nlm.nih.gov/pubmed/20038812
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI40801
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