Načítá se...

Congenital Bone Fractures in Spinal Muscular Atrophy: Functional Role for SMN Protein in Bone Remodeling

Spinal muscular atrophy is the second most common fatal childhood disorder. Core clinical features include muscle weakness caused by degenerating lower motor neurons and a high incidence of bone fractures and hypercalcemia. Fractures further compromise quality of life by progression of joint contrac...

Celý popis

Uloženo v:
Podrobná bibliografie
Hlavní autoři: Shanmugarajan, Srinivasan, Swoboda, Kathryn J., Iannaccone, Susan T., Ries, William L., Maria, Bernard L., Reddy, Sakamuri V.
Médium: Artigo
Jazyk:Inglês
Vydáno: 2007
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC2787099/
https://ncbi.nlm.nih.gov/pubmed/17761651
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/0883073807305664
Tagy: Přidat tag
Žádné tagy, Buďte první, kdo otaguje tento záznam!