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Intermediate Filament Diseases: Desminopathy

Desminopathy is one of the most common intermediate filament human disorders associated with mutations in closely interacting proteins, desmin and alphaB-crystallin. The inheritance pattern in familial desminopathy is characterized as autosomal dominant or autosomal recessive, but many cases have no...

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Autors principals: Goldfarb, Lev G., Olivé, Montse, Vicart, Patrick, Goebel, Hans H.
Format: Artigo
Idioma:Inglês
Publicat: 2008
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2776705/
https://ncbi.nlm.nih.gov/pubmed/19181099
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