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Use of Rituximab for Refractory Cytopenias Associated with Autoimmune Lymphoproliferative Syndrome (ALPS)

BACKGROUND: ALPS is a disorder of apoptosis resulting in accumulation of autoreactive lymphocytes, leading to marked lymphadenopathy, hepatosplenomegaly and multilineage cytopenias due to splenic sequestration and/or autoimmune destruction often presenting in childhood. We summarize our experience o...

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Hlavní autoři: Rao, V. Koneti, Price, Susan, Perkins, Katie, Aldridge, Patricia, Tretler, Jean, Davis, Joie, Dale, Janet K., Gill, Fred, Hartman, Kip R., Stork, Linda C., Gnarra, David J., Krishnamurti, Lakshmanan, Newburger, Peter E., Puck, Jennifer, Fleisher, Thomas
Médium: Artigo
Jazyk:Inglês
Vydáno: 2009
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On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC2774763/
https://ncbi.nlm.nih.gov/pubmed/19214977
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/pbc.21965
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