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Approaches to Managing Autoimmune Cytopenias in Novel Immunological Disorders with Genetic Underpinnings Like Autoimmune Lymphoproliferative Syndrome

Autoimmune lymphoproliferative syndrome (ALPS) is a rare disorder of apoptosis. It is frequently caused by mutations in FAS (TNFRSF6) gene. Unlike most of the self-limiting autoimmune cytopenias sporadically seen in childhood, multi lineage cytopenias due to ALPS are often refractory, as their inher...

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Dettagli Bibliografici
Pubblicato in:Front Pediatr
Autore principale: Rao, V. Koneti
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4508836/
https://ncbi.nlm.nih.gov/pubmed/26258116
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fped.2015.00065
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