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Decreased Nitric Oxide Bioavailability in a Mouse Model of Fabry Disease

Fabry disease is a lysosomal storage disorder that results in an accumulation of globotriaosylceramide in vascular tissue secondary to a deficiency in α-galactosidase A. The glycolipid-associated vasculopathy results in strokes and cardiac disease, but the basis for these complications is poorly und...

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Hlavní autoři: Shu, Liming, Park, James L., Byun, Jaeman, Pennathur, Subramaniam, Kollmeyer, Jessica, Shayman, James A.
Médium: Artigo
Jazyk:Inglês
Vydáno: American Society of Nephrology 2009
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC2736776/
https://ncbi.nlm.nih.gov/pubmed/19628671
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1681/ASN.2008111190
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