Cargando...

Deficiency of the E3 ubiquitin ligase TRIM32 in mice leads to a myopathy with a neurogenic component

Limb-girdle muscular dystrophy type 2H (LGMD2H) and sarcotubular myopathy are hereditary skeletal muscle disorders caused by mutations in TRIM32. We previously identified TRIM32 as an E3 ubiquitin ligase that binds to myosin and ubiquitinates actin. To date four TRIM32 mutations have been linked to...

Descripción completa

Guardado en:
Detalles Bibliográficos
Autores principales: Kudryashova, Elena, Wu, Jun, Havton, Leif A., Spencer, Melissa J.
Formato: Artigo
Lenguaje:Inglês
Publicado: Oxford University Press 2009
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2722196/
https://ncbi.nlm.nih.gov/pubmed/19155210
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddp036
Etiquetas: Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!