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Tragedy in a heartbeat: malfunctioning desmin causes skeletal and cardiac muscle disease

Muscle fiber deterioration resulting in progressive skeletal muscle weakness, heart failure, and respiratory distress occurs in more than 20 inherited myopathies. As discussed in this Review, one of the newly identified myopathies is desminopathy, a disease caused by dysfunctional mutations in desmi...

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Detaylı Bibliyografya
Asıl Yazarlar: Goldfarb, Lev G., Dalakas, Marinos C.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: American Society for Clinical Investigation 2009
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC2701871/
https://ncbi.nlm.nih.gov/pubmed/19587455
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI38027
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