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The fate of intravenously administered tetrahydrobiopterin and its implications for heterologous gene therapy of phenylketonuria

Tetrahydrobiopterin (BH(4)) is a required cofactor for the enzymatic activity of phenylalanine hydroxylase (PAH) and is synthesized de novo from GTP in several tissues. Heterologous expression of PAH in tissues other than liver is a potential novel therapy for human phenylketonuria that is completel...

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Détails bibliographiques
Auteurs principaux: Harding, Cary O., Neff, Mark, Wild, Krzysztof, Jones, Kelly, Elzaouk, Lina, Thöny, Beat, Milstien, Sheldon
Format: Artigo
Langue:Inglês
Publié: 2004
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC2694038/
https://ncbi.nlm.nih.gov/pubmed/14728991
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ymgme.2003.10.002
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