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Multiple congenital malformations of Wolf-Hirschhorn syndrome are recapitulated in Fgfrl1 null mice

Wolf-Hirschhorn syndrome (WHS) is caused by deletions in the short arm of chromosome 4 (4p) and occurs in about one per 20,000 births. Patients with WHS display a set of highly variable characteristics including craniofacial dysgenesis, mental retardation, speech problems, congenital heart defects,...

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Autori principali: Catela, Catarina, Bilbao-Cortes, Daniel, Slonimsky, Esfir, Kratsios, Paschalis, Rosenthal, Nadia, te Welscher, Pascal
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Company of Biologists Limited 2009
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2675798/
https://ncbi.nlm.nih.gov/pubmed/19383940
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1242/dmm.002287
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