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Molecular Pathology of Human Prion Diseases

Prion diseases are fatal neurodegenerative conditions in humans and animals. In this review, we summarize the molecular background of phenotypic variability, relation of prion protein (PrP) to other proteins associated with neurodegenerative diseases, and pathogenesis of neuronal vulnerability. PrP...

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Autors principals: Kovacs, Gabor G., Budka, Herbert
Format: Artigo
Idioma:Inglês
Publicat: Molecular Diversity Preservation International (MDPI) 2009
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2672014/
https://ncbi.nlm.nih.gov/pubmed/19399233
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms10030976
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