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Impaired ERAD and ER stress are early and specific events in polyglutamine toxicity

Protein misfolding, whether caused by aging, environmental factors, or genetic mutations, is a common basis for neurodegenerative diseases. The misfolding of proteins with abnormally long polyglutamine (polyQ) expansions causes several neurodegenerative disorders, such as Huntington’s disease (HD)....

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Detalhes bibliográficos
Main Authors: Duennwald, Martin L., Lindquist, Susan
Formato: Artigo
Idioma:Inglês
Publicado em: Cold Spring Harbor Laboratory Press 2008
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2600758/
https://ncbi.nlm.nih.gov/pubmed/19015277
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1101/gad.1673408
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