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Bile composition in Alagille Syndrome and PFIC patients having Partial External Biliary Diversion

BACKGROUND: Partial External Biliary Diversion (PEBD) is a surgical intervention to treat children with Progressive Familial Intrahepatic Cholestasis (PFIC) and Alagille syndrome (AGS). PEBD can reduce disease progression, and examining the alterations in biliary lipid composition may be a prognosti...

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Autors principals: Emerick, Karan M, Elias, Marc S, Melin-Aldana, Hector, Strautnieks, Sandra, Thompson, Richard J, Bull, Laura N, Knisely, AS, Whitington, Peter F, Green, Richard M
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2008
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2585081/
https://ncbi.nlm.nih.gov/pubmed/18937870
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1471-230X-8-47
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