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Epidermolysis bullosa. I. Molecular genetics of the junctional and hemidesmosomal variants

INTRODUCTION: Epidermolysis bullosa (EB), a group of autosomal heritable blistering diseases, is characterised by extensive phenotypic variability with considerable morbidity and mortality. EB is classified into distinct subtypes depending on the location of blistering within the cutaneous dermoepid...

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Autors principals: Varki, R, Sadowski, S, Pfendner, E, Uitto, J
Format: Artigo
Idioma:Inglês
Publicat: BMJ Group 2006
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2564586/
https://ncbi.nlm.nih.gov/pubmed/16473856
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/jmg.2005.039685
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