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Isofagomine- and 2,5-Anhydro-2,5-Imino-D-Glucitol-Based Glucocerebrosidase Pharmacological Chaperones for Gaucher Disease Intervention

Gaucher disease, resulting from deficient lysosomal glucocerebrosidase (GC) activity, is the most common lysosomal storage disorder. Clinically important GC mutant enzymes typically have reduced specific activity and reduced lysosomal concentration, the latter due to compromised folding and traffick...

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Bibliografiska uppgifter
Huvudupphovsmän: Yu, Zhanqian, Sawkar, Anu R., Whalen, Lisa J., Wong, Chi-Huey, Kelly, Jeffery W.
Materialtyp: Artigo
Språk:Inglês
Publicerad: 2007
Ämnen:
Länkar:https://ncbi.nlm.nih.gov/pmc/articles/PMC2543937/
https://ncbi.nlm.nih.gov/pubmed/17201413
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1021/jm060677i
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