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Abnormal dendritic spines in fragile X knockout mice: Maturation and pruning deficits

Fragile X syndrome arises from blocked expression of the fragile X mental retardation protein (FMRP). Golgi-impregnated mature cerebral cortex from fragile X patients exhibits long, thin, tortuous postsynaptic spines resembling spines observed during normal early neocortical development. Here we des...

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Publicat a:Proc Natl Acad Sci U S A
Autors principals: Comery, Thomas A., Harris, Jennifer B., Willems, Patrick J., Oostra, Ben A., Irwin, Scott A., Weiler, Ivan Jeanne, Greenough, William T.
Format: Artigo
Idioma:Inglês
Publicat: National Academy of Sciences 1997
Matèries:
Accés en línia:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC24690/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/9144249/
https://ncbi.nlm.nih.govhttps://doi.org/10.1073/pnas.94.10.5401
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