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Von Willebrand factor, ADAMTS13, and thrombotic thrombocytopenic purpura

Discoveries during the past decade have revolutionized our understanding of idiopathic thrombotic thrombocytopenic purpura (TTP). Most cases in adults are caused by acquired autoantibodies that inhibit ADAMTS13, a metalloprotease that cleaves von Willebrand factor within nascent platelet-rich thromb...

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Detalles Bibliográficos
Autor principal: Sadler, J. Evan
Formato: Artigo
Lenguaje:Inglês
Publicado: American Society of Hematology 2008
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2435681/
https://ncbi.nlm.nih.gov/pubmed/18574040
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/blood-2008-02-078170
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