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Myofilament Degradation and Dysfunction of Human Cardiomyocytes in Fabry Disease

Early detection of myocardial dysfunction in Fabry disease (FD) cardiomyopathy suggests the contribution of myofilament structural alterations. Six males with untreated FD cardiomyopathy submitted to cardiac studies, including tissue Doppler imaging and left ventricular endomyocardial biopsy. Active...

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Detaylı Bibliyografya
Asıl Yazarlar: Chimenti, Cristina, Hamdani, Nazha, Boontje, Nicky M., DeCobelli, Francesco, Esposito, Antonio, Bronzwaer, Jean G.F., Stienen, Ger J.M., Russo, Matteo A., Paulus, Walter J., Frustaci, Andrea, van der Velden, Jolanda
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: American Society for Investigative Pathology 2008
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC2408409/
https://ncbi.nlm.nih.gov/pubmed/18467700
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2353/ajpath.2008.070576
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