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Functional Wnt Signaling Is Increased in Idiopathic Pulmonary Fibrosis

BACKGROUND: Idiopathic pulmonary fibrosis (IPF) is a fatal lung disease, characterized by distorted lung architecture and loss of respiratory function. Alveolar epithelial cell injury and hyperplasia, enhanced extracellular matrix deposition, and (myo)fibroblast activation are features of IPF. Wnt/β...

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Autori principali: Königshoff, Melanie, Balsara, Nisha, Pfaff, Eva-Maria, Kramer, Monika, Chrobak, Izabella, Seeger, Werner, Eickelberg, Oliver
Natura: Artigo
Lingua:Inglês
Pubblicazione: Public Library of Science 2008
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2374879/
https://ncbi.nlm.nih.gov/pubmed/18478089
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0002142
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