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Impaired ubiquitin–proteasome system activity in the synapses of Huntington's disease mice

Huntington's disease (HD) is caused by the expansion of a polyglutamine tract in the N-terminal region of huntingtin (htt) and is characterized by selective neurodegeneration. In addition to forming nuclear aggregates, mutant htt accumulates in neuronal processes as well as synapses and affects...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Wang, Jianjun, Wang, Chuan-En, Orr, Adam, Tydlacka, Suzanne, Li, Shi-Hua, Li, Xiao-Jiang
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: The Rockefeller University Press 2008
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC2290845/
https://ncbi.nlm.nih.gov/pubmed/18362179
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.200709080
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