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Retarded protein folding of deficient human α(1)-antitrypsin D256V and L41P variants

α(1)-Antitrypsin is the most abundant protease inhibitor in plasma and is the archetype of the serine protease inhibitor superfamily. Genetic variants of human α(1)-antitrypsin are associated with early-onset emphysema and liver cirrhosis. However, the detailed molecular mechanism for the pathogenic...

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Main Authors: Jung, Chan-Hun, Na, Yu-Ran, Im, Hana
Formato: Artigo
Idioma:Inglês
Publicado: Cold Spring Harbor Laboratory Press 2004
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC2286720/
https://ncbi.nlm.nih.gov/pubmed/14767073
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1110/ps.03356604
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