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Mice lacking complex gangliosides develop Wallerian degeneration and myelination defects

Gangliosides are a family of sialic acid-containing glycosphingolipids highly enriched in the mammalian nervous system. Although they are the major sialoglycoconjugates in the brain, their neurobiological functions remain poorly defined. By disrupting the gene for a key enzyme in complex ganglioside...

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Autors principals: Sheikh, Kazim A., Sun, Ji, Liu, Yujing, Kawai, Hiromichi, Crawford, Thomas O., Proia, Richard L., Griffin, John W., Schnaar, Ronald L.
Format: Artigo
Idioma:Inglês
Publicat: The National Academy of Sciences 1999
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC22120/
https://ncbi.nlm.nih.gov/pubmed/10377449
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