A carregar...

Pyridoxine‐dependent seizures in Dutch patients: diagnosis by elevated urinary alpha‐aminoadipic semialdehyde levels

BACKGROUND: Pyridoxine‐dependent seizures (PDS) is a rare, autosomal recessively inherited disorder. Recently α‐aminoadipic semialdehyde (α‐AASA) dehydrogenase deficiency was identified as a major cause of PDS, which causes accumulation of both α‐AASA and pipecolic acid (PA) in body fluids. METHODS:...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Main Authors: Bok, Levinus A, Struys, Eduard, Willemsen, Michel A A P, Been, Jasper V, Jakobs, Cornelis
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Group 2007
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2083882/
https://ncbi.nlm.nih.gov/pubmed/17088338
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/adc.2006.103192
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!