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Hindlimb Motor Neurons Require Cu/Zn Superoxide Dismutase for Maintenance of Neuromuscular Junctions

The role of oxidative damage in neurodegenerative disease was investigated in mice lacking cytoplasmic Cu/Zn superoxide dismutase (SOD), created by deletion of the SOD1 gene (SOD1(−/−)). SOD1(−/−) mice developed a chronic peripheral hindlimb axonopathy. Mild denervation of muscle was detected at 2 m...

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Détails bibliographiques
Auteurs principaux: Flood, Dorothy G., Reaume, Andrew G., Gruner, John A., Hoffman, Eric K., Hirsch, James D., Lin, Yin-Guo, Dorfman, Karen S., Scott, Richard W.
Format: Artigo
Langue:Inglês
Publié: American Society for Investigative Pathology 1999
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Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC1866863/
https://ncbi.nlm.nih.gov/pubmed/10433959
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