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Amyloid-β Deposition in Skeletal Muscle of Transgenic Mice : Possible Model of Inclusion Body Myopathy

Inclusion body myopathy is a progressive muscle disorder characterized by nuclear and cytoplasmic inclusions and vacuolation of muscle fibers. Affected muscle fibers contain deposits of congophilic amyloid, amyloid-β immunoreactive filaments, and paired helical filaments, all of which are pathologic...

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Autors principals: Fukuchi, Ken-ichiro, Pham, Dao, Hart, Michael, Li, Ling, Lindsey, J. Russell
Format: Artigo
Idioma:Inglês
Publicat: American Society for Investigative Pathology 1998
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1866340/
https://ncbi.nlm.nih.gov/pubmed/9846958
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