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Activation of MAPK pathways links LMNA mutations to cardiomyopathy in Emery-Dreifuss muscular dystrophy

Mutations in LMNA, which encodes nuclear Lamins A and C cause diseases affecting various organs, including the heart. We have determined the effects of an Lmna H222P mutation on signaling pathways involved in the development of cardiomyopathy in a knockin mouse model of autosomal dominant Emery-Drei...

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Hlavní autoři: Muchir, Antoine, Pavlidis, Paul, Decostre, Valérie, Herron, Alan J., Arimura, Takuro, Bonne, Gisèle, Worman, Howard J.
Médium: Artigo
Jazyk:Inglês
Vydáno: American Society for Clinical Investigation 2007
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On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC1849984/
https://ncbi.nlm.nih.gov/pubmed/17446932
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI29042
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