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Smoking as an aetiological factor in a pedigree with Leber's hereditary optic neuropathy

BACKGROUND/AIMS—Leber's hereditary optic neuropathy (LHON) is a mitochondrial DNA mediated disease which causes severe visual deficits. Although expressivity of the disease is 100%, penetrance is variable, and environmental factors may influence risk of becoming symptomatic. The causative relat...

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Autors principals: Tsao, K., Aitken, P., Johns, D.
Format: Artigo
Idioma:Inglês
Publicat: BMJ Group 1999
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1723036/
https://ncbi.nlm.nih.gov/pubmed/10216058
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