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Hermansky–Pudlak syndrome: infrequent bleeding and first report of Turkish and Pakistani kindreds

Hermansky–Pudlak syndrome (HPS) is a rare disorder characterised by oculocutaneous albinism, a bleeding tendency, and lipofuscinosis. This retrospective study reviews the clinical history and haematological features of 23 cases of HPS. Information was gathered from patient notes and by direct interv...

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Detalles Bibliográficos
Main Authors: Harrison, C, Khair, K, Baxter, B, Russell-Eggitt, I, Hann, I, Liesner, R
Formato: Artigo
Idioma:Inglês
Publicado: 2002
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC1719163/
https://ncbi.nlm.nih.gov/pubmed/11919112
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/adc.86.4.297
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