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Increased persistent Na(+) current and its effect on excitability in motoneurones cultured from mutant SOD1 mice

Mutations in the enzyme superoxide dismutase 1 (SOD1) initiate a progressive motoneurone degeneration in amyotrophic lateral sclerosis (ALS). Transgenic mice overexpressing this mutation develop a similar progressive motoneurone degeneration. In spinal motoneurones cultured from presymptomatic mice...

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Autors principals: Kuo, JJ, Siddique, T, Fu, R, Heckman, CJ
Format: Artigo
Idioma:Inglês
Publicat: Blackwell Science Inc 2005
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1665614/
https://ncbi.nlm.nih.gov/pubmed/15649979
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1113/jphysiol.2004.074138
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