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Mutational analysis of DJ-1 in Drosophila implicates functional inactivation by oxidative damage and aging

Inherited mutations in PARK7, the gene encoding DJ-1, are associated with loss of protein function and early-onset parkinsonism. Like human DJ-1 (hDJ-1), Drosophila DJ-1b protects against oxidative insult and is modified with oxidation. We demonstrate that hDJ-1 rescues flies mutant for DJ-1b, and t...

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Autors principals: Meulener, Marc C., Xu, Kexiang, Thomson, Leonor, Ischiropoulos, Harry, Bonini, Nancy M.
Format: Artigo
Idioma:Inglês
Publicat: National Academy of Sciences 2006
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1533799/
https://ncbi.nlm.nih.gov/pubmed/16894167
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0601891103
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