Загрузка...

Systemic inflammation in glucocerebrosidase-deficient mice with minimal glucosylceramide storage

Gaucher disease, the most common lysosomal storage disease, is caused by a deficiency of glucocerebrosidase resulting in the impairment of glucosylceramide degradation. The hallmark of the disease is the presence of the Gaucher cell, a macrophage containing much of the stored glucosylceramide found...

Полное описание

Сохранить в:
Библиографические подробности
Главные авторы: Mizukami, Hiroki, Mi, Yide, Wada, Ryuichi, Kono, Mari, Yamashita, Tadashi, Liu, Yujing, Werth, Norbert, Sandhoff, Roger, Sandhoff, Konrad, Proia, Richard L.
Формат: Artigo
Язык:Inglês
Опубликовано: American Society for Clinical Investigation 2002
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC150961/
https://ncbi.nlm.nih.gov/pubmed/11994410
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI14530
Метки: Добавить метку
Нет меток, Требуется 1-ая метка записи!