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Transcriptional induction of slit diaphragm genes by Lmx1b is required in podocyte differentiation
LMX1B encodes a LIM-homeodomain transcription factor. Mutations in LMX1B cause nail-patella syndrome (NPS), an autosomal dominant disease with skeletal abnormalities, nail hypoplasia, and nephropathy. Expression of glomerular basement membrane (GBM) collagens is reduced in Lmx1b(–/–) mice, suggestin...
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| Principais autores: | , , , , , , |
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| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
American Society for Clinical Investigation
2002
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| Assuntos: | |
| Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC150942/ https://ncbi.nlm.nih.gov/pubmed/11956244 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI13954 |
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