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Neurospora Strains Harboring Mitochondrial Disease-Associated Mutations in Iron-Sulfur Subunits of Complex I

We subjected the genes encoding the 19.3-, 21.3c-, and 51-kDa iron-sulfur subunits of respiratory chain complex I from Neurospora crassa to site-directed mutagenesis to mimic mutations in human complex I subunits associated with mitochondrial diseases. The V135M substitution was introduced into the...

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Autors principals: Duarte, Margarida, Schulte, Ulrich, Ushakova, Alexandra V., Videira, Arnaldo
Format: Artigo
Idioma:Inglês
Publicat: Copyright © 2005 by the Genetics Society of America 2005
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1456533/
https://ncbi.nlm.nih.gov/pubmed/15956670
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1534/genetics.105.041517
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