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Lamin A/C and emerin are critical for skeletal muscle satellite cell differentiation

Mutations within LMNA, encoding A-type nuclear lamins, are associated with multiple tissue-specific diseases, including Emery-Dreifuss (EDMD2/3) and Limb-Girdle muscular dystrophy (LGMD1B). X-linked EDMD results from mutations in emerin, a lamin A-associated protein. The mechanisms through which the...

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Detalhes bibliográficos
Main Authors: Frock, Richard L., Kudlow, Brian A., Evans, Angela M., Jameson, Samantha A., Hauschka, Stephen D., Kennedy, Brian K.
Formato: Artigo
Idioma:Inglês
Publicado em: Cold Spring Harbor Laboratory Press 2006
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC1369050/
https://ncbi.nlm.nih.gov/pubmed/16481476
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1101/gad.1364906
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