Chargement en cours...

Expression of mutant human cystathionine beta-synthase rescues neonatal lethality but not homocystinuria in a mouse model

Cystathionine β-synthase (CBS) deficiency is a recessive genetic disorder in humans characterized by elevated levels in total plasma homocysteine (tHcy) and frequent thrombosis in humans. The I278T mutation is the most common mutation found in human CBS deficient patients. The T424N mutation was ide...

Description complète

Enregistré dans:
Détails bibliographiques
Auteurs principaux: Wang, Liqun, Chen, Xulin, Tang, Baiqing, Hua, Xiang, Klein-Szanto, Andres, Kruger, Warren D.
Format: Artigo
Langue:Inglês
Publié: 2005
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC1283068/
https://ncbi.nlm.nih.gov/pubmed/15972722
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddi224
Tags: Ajouter un tag
Pas de tags, Soyez le premier à ajouter un tag!