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Tiglicaciduria in propionicacidaemia

Tiglic acid, which has not previously been found in human body fluids, was recently detected in the urine of two patients with propionicacidaemia. These patients had a documented defect in the oxidation of propionate. A competition between acrylyl-CoA and tiglyl-CoA for crotonase could explain the a...

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Библиографические подробности
Главные авторы: Nyhan, William L., Ando, Toshiyuki, Rasmussen, Karsten, Wadlington, William, Kilroy, Anthony W., Cottom, Dennis, Hull, David
Формат: Artigo
Язык:Inglês
Опубликовано: 1972
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC1178511/
https://ncbi.nlm.nih.gov/pubmed/5073234
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