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'Pseudo-dominant' inheritance in Friedreich's ataxia.

A family is described in which Friedreich's ataxia occurred in two generations. It is proposed that this resulted from a homozygote-heterozygote mating. The heterozygote frequency for the Friedreich's ataxia gene is in the order of 1 in 110, so the likelihood of the disease developing in a...

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Dettagli Bibliografici
Autori principali: Harding, A E, Zilkha, K J
Natura: Artigo
Lingua:Inglês
Pubblicazione: 1981
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC1048733/
https://ncbi.nlm.nih.gov/pubmed/7277422
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