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Deep Vein Thrombosis, Raynaud's Phenomenon, and Prinzmetal Angina in a Patient with Glanzmann Thrombasthenia

Patients with Glanzmann thrombasthenia fail to form large platelet thrombi due to mutations that affect the biosynthesis and/or function of the αIIbβ3 integrin. The result is a moderate to severe bleeding syndrome. We now report unusual vascular behaviour in a 55-year-old woman with classic type I d...

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Autores principales: Alan Nurden, Patrick Mercié, Pascal Zely, Paquita Nurden
Formato: Artigo
Lenguaje:Inglês
Publicado: Hindawi Limited 2012-01-01
Colección:Case Reports in Hematology
Acceso en línea:http://dx.doi.org/10.1155/2012/156290
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