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Chaperone networks: Tipping the balance in protein folding diseases

Adult-onset neurodegeneration and other protein conformational diseases are associated with the appearance, persistence, and accumulation of misfolded and aggregation-prone proteins. To protect the proteome from long-term damage, the cell expresses a highly integrated protein homeostasis (proteostas...

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Autors principals: Cindy Voisine, Jesper Søndergaard Pedersen, Richard I. Morimoto
Format: Artigo
Idioma:Inglês
Publicat: Elsevier 2010-10-01
Col·lecció:Neurobiology of Disease
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Accés en línia:http://www.sciencedirect.com/science/article/pii/S0969996110001580
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