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Hyper IgE (Job's) Syndrome: A Primary Immune Deficiency with Oral Manifestations

Hyper-immunoglobulin E syndrome (HIES), also known as Job's syndrome, is a rare primary immunodeficiency disorder characterized by a classic triad: elevated immunoglobulin E (IgE) levels, recurrent pneumonia with pneumatocele formation, and recurrent cold skin abscesses. Case A 5-year-old girl wa...

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Principais autores: Mohammad Esmaeilzadeh, Ali Asghar Soleymani, Sedigheh Mozafar, Navid Tariverdi, Seyed Ali Fatemi, Mahta Khosrozamiri
Formato: Artigo
Idioma:Inglês
Publicado em: Shahid Beheshti University of Medical Sciences 2024-10-01
coleção:Journal of Dental School
Assuntos:
Acesso em linha:https://journals.sbmu.ac.ir/dentistry/article/view/45398
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