Hyper IgE (Job's) Syndrome: A Primary Immune Deficiency with Oral Manifestations
Hyper-immunoglobulin E syndrome (HIES), also known as Job's syndrome, is a rare primary immunodeficiency disorder characterized by a classic triad: elevated immunoglobulin E (IgE) levels, recurrent pneumonia with pneumatocele formation, and recurrent cold skin abscesses. Case A 5-year-old girl wa...
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| Автори: | , , , , , |
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| Формат: | Artigo |
| Мова: | Inglês |
| Опубліковано: |
Shahid Beheshti University of Medical Sciences
2024-10-01
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| Серія: | Journal of Dental School |
| Предмети: | |
| Онлайн доступ: | https://journals.sbmu.ac.ir/dentistry/article/view/45398 |
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